Fulminant systemic capillary leak syndrome due to C1 inhibitor deficiency complicating acute dermatomyositis: a case report
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چکیده
منابع مشابه
Fulminant systemic capillary leak syndrome due to C1 inhibitor deficiency complicating acute dermatomyositis: a case report
INTRODUCTION Dermatomyositis is a chronic inflammatory disorder characterized by muscular and dermatologic symptoms with variable internal organ involvement. This is the first report on a patient with acute dermatomyositis and fulminant systemic capillary leak syndrome. CASE PRESENTATION A 69-year-old Caucasian woman with chronic dermatomyositis presented with clinical signs of severe hypovol...
متن کاملTitle:fulminant Systemic Capillary Leak Syndrome Due to C1 Inhibitor Deficiency Complicating Acute Dermatomyositis: a Case Report
Author's response to reviews: see over We thank the reviewer for his renewed constructive and challenging questions! They brought the solution to our case and further improved the manuscript.
متن کاملSystemic capillary leak syndrome. Case report.
We here report the case of a patient with systemic capillary leak syndrome (SCLS). This syndrome is a rare condition characterized by recurrent episodes of hypotension with hemoconcentration and hypoproteinemia. It is due to unexplained episodic capillary hyperpermeabilty that results in fluid and protein shift from the intravascular to the interstitial space: generalized edema, shock and renal...
متن کاملidiopathic systemic capillary leak syndrome: a case report
conclusions the early signs and symptoms of iscls may be subtle; therefore the diagnosis can easily be missed and prompt treatment of the syndrome may be postponed. thus, the clinician must consider iscls in differential diagnosis in cases of hypotension, hemoconcentration, and hypoalbuminemia. case presentation we present a 58-year-old female who presented with peripheral edema, leg pain, and ...
متن کاملIdiopathic Systemic Capillary Leak Syndrome: A Case Report
Systemic capillary leak syndrome (SCLS) is characterized by recurrent hypovolemic shock associated with edema, hemoconcentration and paradoxal hypoprotidemia due to leakage into the interstitial space. We report a new case with cardiac involvement. A 62-year-old man had two recurrent hypovolemic shocks with SCLS's criteria, associated twice with cardiac systolic dysfunction and atrial fibrillat...
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ژورنال
عنوان ژورنال: Journal of Medical Case Reports
سال: 2014
ISSN: 1752-1947
DOI: 10.1186/1752-1947-8-28